Oui, les patients peuvent éprouver de l'anxiété ou de la dépression en raison de la maladie.
Santé mentaleFibromatoseComplications
#5
Les déformations sont-elles réversibles ?
Les déformations peuvent être partiellement corrigées par la chirurgie, mais pas toujours complètement.
DéformationsChirurgieFibromatose agressive
Facteurs de risque
5
#1
Quels sont les principaux facteurs de risque ?
Les antécédents familiaux et les traumatismes locaux sont des facteurs de risque connus.
Facteurs de risqueFibromatoseAntécédents familiaux
#2
Les femmes sont-elles plus à risque ?
Il n'y a pas de preuve claire que le sexe influence le risque de fibromatose agressive.
Facteurs de risqueFibromatoseSexe
#3
Les personnes jeunes sont-elles plus touchées ?
La fibromatose agressive peut survenir à tout âge, mais elle est plus fréquente chez les jeunes adultes.
Fibromatose agressiveÂgeFacteurs de risque
#4
Les antécédents médicaux influencent-ils le risque ?
Oui, des antécédents de tumeurs ou de maladies des tissus mous peuvent augmenter le risque.
Antécédents médicauxFibromatoseFacteurs de risque
#5
Les traitements antérieurs augmentent-ils le risque ?
Certaines interventions chirurgicales peuvent augmenter le risque de développer une fibromatose.
Traitements antérieursFibromatose agressiveFacteurs de risque
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"@type": "Question",
"name": "Y a-t-il des traitements médicamenteux ?",
"position": 20,
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"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
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"@type": "Answer",
"text": "Les complications incluent des récidives, des douleurs chroniques et des déformations."
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"@type": "Question",
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"@type": "Question",
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"position": 26,
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"position": 27,
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"@type": "Question",
"name": "Les personnes jeunes sont-elles plus touchées ?",
"position": 28,
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"@type": "Answer",
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"@type": "Question",
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"position": 29,
"acceptedAnswer": {
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"@type": "Question",
"name": "Les traitements antérieurs augmentent-ils le risque ?",
"position": 30,
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"@type": "Answer",
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Department for Radiology and Neuroradiology, University Hospital Schleswig-Holstein, Campus Kiel, Germany; Institute of Diagnostic and Interventional Radiology and Nuclear Medicine, University Hospital Bergmannsheil, Bochum, Germany. Electronic address: Sam.Sedaghat@uksh.de.
Department for Radiology and Neuroradiology, University Hospital Schleswig-Holstein, Campus Kiel, Germany; Institute of Diagnostic and Interventional Radiology and Nuclear Medicine, University Hospital Bergmannsheil, Bochum, Germany.
Institute of Diagnostic and Interventional Radiology and Neuroradiology, University Hospital Essen, Germany; Department for Interventional Radiology and Neuroradiology, Klinikum Hochsauerland, Arnsberg, Germany.
Aggressive fibromatosis, histologically classified as benign due to the absence of metastasis, is characterised by locally invasive and destructive growth with high recurrence rates after resection. F...
Deep fibromatosis is a locally aggressive neoplasm commonly involving the extremities. Several authors have described imaging features and complications associated with deep fibromatosis. We present t...
BACKGROUND Desmoid tumors are a fibroblastic proliferation of soft tissues, with an extreme inclination for local dissemination and recurrence. Surgical excision is the usual treatment choice, with da...
Desmoid-type fibromatosis (DF) is a soft tissue tumor characterized by infiltrative growth and a tendency toward local recurrence, while it exhibits self-limiting behavior and shows spontaneous regres...
Desmoid fibromatosis is a myofibroblastic neoplasm of intermediate biologic potential, which has a strong predilection for local recurrence but does not metastasize. Arranged in long, sweeping fascicl...
To report the first UK experience of cryoablation in desmoid fibromatosis (DF) with particular focus on technique, safety, and efficacy....
Patients were selected at multidisciplinary tumour board meetings at a specialist cancer hospital. Radiation dose, procedure duration, and number of cryoprobes were compared for small versus large tum...
Thirteen procedures were performed in 10 patients (eight women, median age 51 years, IQR 42-69 years) between February 2019 and August 2021. Procedures for large tumours had higher radiation dose (2,0...
Cryoablation for symptomatic DF is a reproducible technique with low, transient toxicity, where one or two treatments can achieve a meaningful response. Where possible, the ablation ice ball should fu...
To retrospectively review the various methods used to treat extra-abdominal desmoid fibromatosis (EDF) at our institution to compare treatment response and complications with those for the emerging op...
A single-center retrospective review was conducted to identify patients with EDF who underwent some form of treatment for EDF in any combination (including medical therapy, surgery, percutaneous ablat...
A total of 41 patients (30 women; mean age, 34 y; range, 18-79 y) were included in the study. The extremities (44%) and back (22%) were the most common locations of EDF. Patients underwent a variety o...
Although further work is needed, the early data in this study offers promising results regarding the clinical application of cryoablation for EDF, which appears safer than radiofrequency ablation and ...
Desmoid-type fibromatosis are rare intermediate tumors in children and adolescents. Owing to local aggressiveness and relapse, systemic treatment for symptomatic advanced or progressive forms is recom...
A retrospective review of young patients (<25 years old) with advanced or progressive desmoid type fibromatosis treated with oral vinorelbine in eight large centers of the Société Française des Cancer...
From 2005 to 2020, 24 patients (median age 13.9 years [range, 1.0-23.0]) received oral vinorelbine. Median number of prior systemic lines of treatment was 1 (range, 0-2), mainly based on intravenous l...
Oral vinorelbine seems to be effective to control advanced or progressive desmoid type fibromatosis in young patients, with a well-tolerated profile. These results support testing this drug as first-l...
A 31-year-old Indian female with a history of near-total thyroidectomy 2.5 years prior presented with recurrent neck swelling. Magnetic resonance imaging (MRI) of the neck revealed an infiltrating mas...
Sinonasal myxoma (SNM) is a rare benign mesenchymal tumor that arises in the sinonasal cavity or maxilla and almost exclusively affects young children. Currently, it is considered a specific entity, b...