Severe immune thrombocytopenia in two patients with systemic sclerosis.


Journal

Joint bone spine
ISSN: 1778-7254
Titre abrégé: Joint Bone Spine
Pays: France
ID NLM: 100938016

Informations de publication

Date de publication:
Jul 2023
Historique:
received: 16 01 2023
revised: 15 02 2023
accepted: 03 03 2023
medline: 26 6 2023
pubmed: 19 3 2023
entrez: 18 3 2023
Statut: ppublish

Résumé

Thrombocytopenia in the context of systemic sclerosis (SSc) is rare. It should primarily raise the possibility of scleroderma renal crisis. Immune thrombocytopenia (ITP) is another cause of low platelets that is common in systemic lupus erythematosus, but tremendously rare in patients with SSc. We herein report two cases of severe ITP in patients with SSc. The first case is a 29-year-old woman with very low platelet counts (2×10

Identifiants

pubmed: 36933783
pii: S1297-319X(23)00039-8
doi: 10.1016/j.jbspin.2023.105560
pii:
doi:

Substances chimiques

Immunoglobulins, Intravenous 0
Rituximab 4F4X42SYQ6

Types de publication

Case Reports

Langues

eng

Sous-ensembles de citation

IM

Pagination

105560

Informations de copyright

Copyright © 2023 Société française de rhumatologie. Published by Elsevier Masson SAS. All rights reserved.

Auteurs

Gonçalo Boleto (G)

Department of Rheumatology, université Paris Cité, Cochin Hospital, Paris, France.

Jérôme Avouac (J)

Department of Rheumatology, université Paris Cité, Cochin Hospital, Paris, France; Inserm U1016, institut Cochin, CNRS UMR8104, Paris, France.

Bertrand Godeau (B)

Centre de référence des cytopénies auto-immunes de l'adulte, service de médecine interne, CHU Henri-Mondor, AP-HP, université Paris-Est Créteil, Créteil, France.

Yannick Allanore (Y)

Department of Rheumatology, université Paris Cité, Cochin Hospital, Paris, France; Inserm U1016, institut Cochin, CNRS UMR8104, Paris, France. Electronic address: yannick.allanore@aphp.fr.

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Classifications MeSH