Performance analysis of AL amyloidosis cardiac biomarker staging systems with special focus on renal failure and atrial arrhythmia.


Journal

Haematologica
ISSN: 1592-8721
Titre abrégé: Haematologica
Pays: Italy
ID NLM: 0417435

Informations de publication

Date de publication:
07 2019
Historique:
received: 26 08 2018
accepted: 15 01 2019
pubmed: 19 1 2019
medline: 3 6 2020
entrez: 19 1 2019
Statut: ppublish

Résumé

Systemic light chain amyloidosis is a rare and life-threatening disorder, for which accurate risk stratification is crucial. Current cardiac staging systems (MAYO2004, MAYO3b, and MAYO2012) are mainly based on biomarkers, which have uncertain reliability in the context of atrial fibrillation, arrhythmia or pacemaker stimulation as well as renal insufficiency. We compared the performance of the established staging systems with particular regard to these comorbidities in 1,224 patients with systemic light chain amyloidosis diagnosed at our center from July 2002 until March 2017. We first characterized the subsets with an estimated glomerular filtration rate <50 mL/min/1.73 m

Identifiants

pubmed: 30655373
pii: haematol.2018.205336
doi: 10.3324/haematol.2018.205336
pmc: PMC6601086
doi:

Substances chimiques

Biomarkers 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

1451-1459

Commentaires et corrections

Type : CommentIn

Informations de copyright

Copyright© 2019 Ferrata Storti Foundation.

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Auteurs

Tobias Dittrich (T)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital.
Amyloidosis Center, Heidelberg University Hospital.
Clinical Cooperation Unit Molecular Hematology/Oncology, German Cancer Research Center (DKFZ) and Department of Internal Medicine V, Heidelberg University Hospital.

Axel Benner (A)

Division of Biostatistics, German Cancer Research Center (DKFZ), Heidelberg.

Christoph Kimmich (C)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital.
Amyloidosis Center, Heidelberg University Hospital.

Fabian Aus dem Siepen (FAD)

Amyloidosis Center, Heidelberg University Hospital.
Department of Internal Medicine III, Division of Cardiology, Heidelberg University Hospital, Germany.

Kaya Veelken (K)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital.
Amyloidosis Center, Heidelberg University Hospital.

Arnt V Kristen (AV)

Amyloidosis Center, Heidelberg University Hospital.
Department of Internal Medicine III, Division of Cardiology, Heidelberg University Hospital, Germany.

Tilmann Bochtler (T)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital.
Amyloidosis Center, Heidelberg University Hospital.
Clinical Cooperation Unit Molecular Hematology/Oncology, German Cancer Research Center (DKFZ) and Department of Internal Medicine V, Heidelberg University Hospital.

Hugo A Katus (HA)

Department of Internal Medicine III, Division of Cardiology, Heidelberg University Hospital, Germany.

Carsten Müller-Tidow (C)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital.
Amyloidosis Center, Heidelberg University Hospital.

Ute Hegenbart (U)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital stefan.schoenland@med.uni-heidelberg.de ute.hegenbart@med.uni-heidelberg.de.
Amyloidosis Center, Heidelberg University Hospital.

Stefan O Schönland (SO)

Department of Internal Medicine V, Division of Hematology/Oncology, Heidelberg University Hospital stefan.schoenland@med.uni-heidelberg.de ute.hegenbart@med.uni-heidelberg.de.
Amyloidosis Center, Heidelberg University Hospital.

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Classifications MeSH