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Malformations et maladies congénitales, héréditaires et néonatales
Malformations
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Cardiopathies congénitales
Malformations des cloisons cardiaques
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Syndrome de Lutembacher
Syndrome de Lutembacher : Questions médicales fréquentes
Diagnostic
5
Syndrome de Lutembacher
Échocardiographie
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5
Essoufflement
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Palpitations
Anomalies de conduction
Insuffisance cardiaque
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5
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5
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Suivi post-opératoire
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5
Insuffisance cardiaque
Arythmie
Arythmies
Sténose mitrale
Gestion des complications
Médicaments
Facteurs de risque
5
Antécédents familiaux
Malformations congénitales
Maladies cardiaques
Antécédents médicaux
Mode de vie sédentaire
Alimentation
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"@type": "Question",
"name": "Quels sont les symptômes principaux du syndrome ?",
"position": 6,
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"name": "Le syndrome provoque-t-il des complications respiratoires ?",
"position": 7,
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"@type": "Question",
"name": "Comment se manifeste la fatigue dans ce syndrome ?",
"position": 8,
"acceptedAnswer": {
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"text": "La fatigue est souvent due à une insuffisance cardiaque liée à la sténose."
}
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"@type": "Question",
"name": "Les palpitations sont-elles fréquentes ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les palpitations sont courantes en raison des anomalies de conduction."
}
},
{
"@type": "Question",
"name": "Y a-t-il des signes d'insuffisance cardiaque ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des signes comme l'œdème des membres inférieurs peuvent apparaître."
}
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{
"@type": "Question",
"name": "Peut-on prévenir le syndrome de Lutembacher ?",
"position": 11,
"acceptedAnswer": {
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"text": "Il n'existe pas de prévention spécifique, mais un suivi cardiaque régulier est conseillé."
}
},
{
"@type": "Question",
"name": "Quels modes de vie peuvent aider à la prévention ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Un mode de vie sain, incluant une alimentation équilibrée et de l'exercice, est bénéfique."
}
},
{
"@type": "Question",
"name": "Les contrôles médicaux réguliers sont-ils importants ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des contrôles réguliers permettent de détecter précocement des anomalies cardiaques."
}
},
{
"@type": "Question",
"name": "Faut-il éviter certains facteurs de risque ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, éviter le tabagisme et l'hypertension peut réduire les risques cardiaques."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles recommandées ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les vaccinations contre la grippe et le pneumocoque sont conseillées."
}
},
{
"@type": "Question",
"name": "Quel est le traitement principal du syndrome de Lutembacher ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement principal est chirurgical, visant à corriger les anomalies cardiaques."
}
},
{
"@type": "Question",
"name": "Des médicaments sont-ils utilisés dans ce syndrome ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des diurétiques et des anticoagulants peuvent être prescrits."
}
},
{
"@type": "Question",
"name": "Quand est-il nécessaire d'intervenir chirurgicalement ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'intervention est nécessaire en cas de symptômes sévères ou de complications."
}
},
{
"@type": "Question",
"name": "Quels sont les risques associés à la chirurgie ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les risques incluent des infections, des saignements et des complications cardiaques."
}
},
{
"@type": "Question",
"name": "Le suivi post-opératoire est-il important ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier est crucial pour surveiller les complications potentielles."
}
},
{
"@type": "Question",
"name": "Quelles sont les complications possibles du syndrome ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent l'insuffisance cardiaque, l'arythmie et l'embolie."
}
},
{
"@type": "Question",
"name": "Comment l'insuffisance cardiaque se manifeste-t-elle ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Elle se manifeste par une dyspnée, une fatigue accrue et un œdème."
}
},
{
"@type": "Question",
"name": "Le syndrome peut-il entraîner un AVC ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le risque d'AVC est augmenté en raison des embolies possibles."
}
},
{
"@type": "Question",
"name": "Les arythmies sont-elles fréquentes ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les arythmies peuvent survenir en raison de la sténose mitrale."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "La gestion inclut des médicaments, un suivi régulier et parfois une intervention chirurgicale."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque du syndrome ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux de maladies cardiaques et des malformations congénitales."
}
},
{
"@type": "Question",
"name": "L'âge influence-t-il le risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le risque augmente avec l'âge, surtout après 50 ans."
}
},
{
"@type": "Question",
"name": "Le sexe joue-t-il un rôle dans ce syndrome ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les femmes sont souvent plus touchées que les hommes."
}
},
{
"@type": "Question",
"name": "Les maladies cardiaques antérieures augmentent-elles le risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des antécédents de maladies cardiaques augmentent le risque de développer ce syndrome."
}
},
{
"@type": "Question",
"name": "Le mode de vie peut-il influencer le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un mode de vie sédentaire et une mauvaise alimentation augmentent le risque."
}
}
]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 26/12/2024
Contenu vérifié selon les dernières recommandations médicales
2 publications dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Yan'an Affiliated Hospital of Kunming Medical University, Kunming, China. 664375047@qq.com.
Publications dans "Syndrome de Lutembacher" :
2 publications dans cette catégorie
Affiliations :
Department of Emergency Medicine, University of Maryland School of Medicine, 110 South Paca Street, 6th Floor, Suite 200, Baltimore, MD 21201, USA. Electronic address: https://twitter.com/LeenAlblaihed.
Publications dans "Syndrome de Lutembacher" :
2 publications dans cette catégorie
Affiliations :
Department of Emergency Medicine, Elisabeth TweeSteden Ziekenhuis, Hilvarenbeekseweg 60, 5022 GC Tilburg, the Netherlands; Department of Emergency Medicine, University of Maryland School of Medicine, MD, USA. Electronic address: m.huisintveld@etz.nl.
Publications dans "Syndrome de Lutembacher" :
2 publications dans cette catégorie
Affiliations :
Zabludowicz Center for Autoimmune Diseases, Chaim Sheba Medical Center, Tel-Hashomer 5265601, Ramat-Gan; Reichmann University, Herzliya, Israel.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Akita University Graduate School of Medicine, Akita, Japan.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Akita University Graduate School of Medicine, Akita, Japan. Electronic address: takuya.wa0610@gmail.com.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Akita University Graduate School of Medicine, Akita, Japan.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Akita University Graduate School of Medicine, Akita, Japan.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Akita University Graduate School of Medicine, Akita, Japan.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Akita University Graduate School of Medicine, Akita, Japan.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Cardiology, KS Hegde Medical Academy, Mangalore, Karnataka, India johnydilip@gmail.com.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Cardiology, KS Hegde Medical Academy, Mangalore, Karnataka, India.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Internal Medicine, KS Hegde Medical Academy, Mangalore, Karnataka, India.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Periodontology, AB Shetty Memorial Institute of Dental Sciences, Mangalore, Karnataka, India.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Yan'an Affiliated Hospital of Kunming Medical University, Kunming, China. ymd0468@126.com.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Yan'an Affiliated Hospital of Kunming Medical University, Kunming, China. 865873583@qq.com.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Yan'an Affiliated Hospital of Kunming Medical University, Kunming, China. 328892428@qq.com.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiovascular Surgery, Yan'an Affiliated Hospital of Kunming Medical University, Kunming, China. wujiankmmu@163.com.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Medicine Kwame Nkrumah University of Science and Technology Kumasi Ghana.
Department of Medicine Komfo Anokye Teaching Hospital Kumasi Ghana.
Publications dans "Syndrome de Lutembacher" :
1 publication dans cette catégorie
Affiliations :
Department of Medicine Komfo Anokye Teaching Hospital Kumasi Ghana.
Department of Physiology Kwame Nkrumah University of Science and Technology Kumasi Ghana.
Publications dans "Syndrome de Lutembacher" :
A woman in her 30s presented with progressive worsening of dyspnoea for 6 months. On evaluation, she was diagnosed with severe rheumatic mitral stenosis (mitral valve area of 0.6 cm...
Lutembacher syndrome (LS) is a rare syndrome comprising a combination of atrial septal defect (ASD) and mitral stenosis. We present the case of a 28-year-old man, who presented with progressively wors...
Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for ...
Lutembacher syndrome (LS), combining atrial septal defect (ASD) and mitral stenosis (MS), is rare, particularly in rural areas. This case presents a 55-year-old Nepalese woman with LS symptoms; howeve...
A 55-year-old woman from rural Nepal presented with 30-day leg swelling and shortness of breath. Apart from autosomal dominant polycystic kidney disease (ADPKD) and smoking, she had no significant com...
LS is rarer in regions with low rheumatic heart disease (RHD) prevalence like Nepal. This case, despite rarity, delayed presentation, and financial barriers, emphasizes early intervention's importance...
This Nepalese LS case highlights its complexity and management challenges, especially in resource-limited settings. It stresses early intervention's importance and the impact of financial constraints ...
Platypnea-orthodeoxia syndrome (POS) is defined by dyspnea and deoxygenation due to a change in body position from lying down to an upright position. We present a case of a large right atrial (RA) thr...
Lutembacher's syndrome refers to the rare combination of atrial septal defect and mitral stenosis. This condition is still underdiagnosed despite its distinct clinical, paraclinical, and therapeutic i...
We report the case of a 60-year-old woman presenting with acute congestive heart failure. Investigations revealed the combination of low-gradient severe rheumatic mitral stenosis and ostium secundum a...
Lutembacher's syndrome continues to be a rare condition in our practice. Once low-gradient severe mitral stenosis is diagnosed, it is essential to search for an associated atrial septal defect, especi...
Atrial septal defect (ASD), whether congenital or iatrogenic, and mitral stenosis (MS), whether congenital or acquired, may all come together into a condition called Lutembacher's syndrome (LS). The A...
Lutembacher's syndrome is a rare disease defined as the combination of atrial septal defect and mitral stenosis, which relieves the progression of symptoms resulting from mitral stenosis. We present a...
Despite the complexity of Lutembacher's syndrome, including the involvement of several deformities and pathological mechanisms of mitral stenosis, sinus venosus type of interatrial defects with partia...
Gorlin syndrome and Cowden syndrome are hereditary diseases that are characterized by multiple malignancies, cutaneous symptoms, and various other abnormalities. Both disorders are caused by a mutatio...
Alport syndrome (AS) is a progressive renal disease characterized by hematuria and progressive renal failure. X-linked dominant (XLAS) is the major inheritance form, accounting for almost 80% of the c...