Novel hybrid silicon-lipid nanoparticles deliver a siRNA to cure autosomal dominant osteopetrosis in mice. Implications for gene therapy in humans.

MT: delivery strategies autosomal dominant osteopetrosis bone resorption delivery nanoparticles genetic bone diseases osteoclasts silicon therapeutic siRNA therapy

Journal

Molecular therapy. Nucleic acids
ISSN: 2162-2531
Titre abrégé: Mol Ther Nucleic Acids
Pays: United States
ID NLM: 101581621

Informations de publication

Date de publication:
12 Sep 2023
Historique:
received: 25 03 2023
accepted: 16 08 2023
medline: 8 9 2023
pubmed: 8 9 2023
entrez: 8 9 2023
Statut: epublish

Résumé

Rare skeletal diseases are still in need of proper clinically available transfection agents as the major challenge for first-in-human translation relates to intrinsic difficulty in targeting bone without exacerbating any inherent toxicity due to used vector. SiSaf's silicon stabilized hybrid lipid nanoparticles (sshLNPs) constitute next-generation non-viral vectors able to retain the integrity and stability of constructs and to accommodate considerable payloads of biologicals, without requiring cold-chain storage. sshLNP was complexed with a small interfering RNA (siRNA) specifically designed against the human

Identifiants

pubmed: 37680985
doi: 10.1016/j.omtn.2023.08.020
pii: S2162-2531(23)00231-7
pmc: PMC10480457
doi:

Types de publication

Journal Article

Langues

eng

Pagination

925-937

Informations de copyright

© 2023 The Author(s).

Déclaration de conflit d'intérêts

A.T. and A.M. served as consultant, P.P had a service agreement, and F.M.S., N.T.-P., P.B.R, C.B., U.N., M.W., and A.D. are scientists working for SiSaf Ltd, a commercial stage biopharmaceutical company. S.S.-S. is founder and CEO of SiSaf Ltd.

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Auteurs

Antonio Maurizi (A)

Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, L'Aquila, Italy.

Piergiorgio Patrizii (P)

Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, L'Aquila, Italy.

Anna Teti (A)

Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, L'Aquila, Italy.

Flavia Maria Sutera (FM)

SiSaf Limited, Guildford, UK.

Paulina Baran-Rachwalska (P)

SiSaf Limited, Guildford, UK.

Chris Burns (C)

PorousSilicon, Salzburg, Austria.

Uttom Nandi (U)

SiSaf Limited, Guildford, UK.

Michael Welsh (M)

SiSaf Limited, Guildford, UK.

Nissim Torabi-Pour (N)

SiSaf Limited, Guildford, UK.

Ashkan Dehsorkhi (A)

SiSaf Limited, Guildford, UK.

Suzanne Saffie-Siebert (S)

SiSaf Limited, Guildford, UK.

Classifications MeSH