Inherited CSNK2A1 variants in families with Okur-Chung neurodevelopmental syndrome.

CSNK2A1 Okur-Chung neurodevelopmental syndrome casein kinase 2 inherited variants variable expressivity

Journal

Clinical genetics
ISSN: 1399-0004
Titre abrégé: Clin Genet
Pays: Denmark
ID NLM: 0253664

Informations de publication

Date de publication:
Nov 2023
Historique:
revised: 12 07 2023
received: 15 06 2023
accepted: 16 07 2023
pubmed: 26 7 2023
medline: 26 7 2023
entrez: 26 7 2023
Statut: ppublish

Résumé

Pedigree showing the autosomal dominant inheritance pattern of CSNK21 variants in families presenting with OCNDS. (A) Maternal inheritance to two daughters in Family 1, (B) Paternal inheritance to a daughter in Family 2, and (C) Maternal inheritance to two sons in Family 3.

Identifiants

pubmed: 37491870
doi: 10.1111/cge.14408
doi:

Types de publication

Letter

Langues

eng

Sous-ensembles de citation

IM

Pagination

607-609

Subventions

Organisme : CSNK2A1 Foundation

Informations de copyright

© 2023 The Authors. Clinical Genetics published by John Wiley & Sons Ltd.

Références

Okur V, Cho MT, Henderson L, et al. De novo mutations in CSNK2A1 are associated with neurodevelopmental abnormalities and dysmorphic features. Hum Genet. 2016;135:699-705. doi:10.1007/s00439-016-1661-y
Jafari Khamirani H, Zoghi S, Motealleh A, et al. Clinical features of Okur-Chung neurodevelopmental syndrome: case report and literature review. Mol Syndromol. 2022;13:381-388.
Chung W, Okur V. Okur-Chung neurodevelopmental syndrome. In: Adam MP, Mirzaa GM, Pagon RA, et al., eds. GeneReviews®. University of Washington; 2022.
Chiu ATG, Pei SLC, Mak CCY, et al. Okur-Chung neurodevelopmental syndrome: eight additional cases with implications on phenotype and genotype expansion. Clin Genet. 2018;93:880-890.
Xu S, Lian Q, Wu J, Li L, Song J. Dual molecular diagnosis of tricho-rhino-phalangeal syndrome type I and Okur-Chung neurodevelopmental syndrome in one Chinese patient: a case report. BMC Med Genet. 2020;21:158.

Auteurs

Newell Belnap (N)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.
Center for Rare Childhood Disorders (C4RCD), Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Aiai Price-Smith (A)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Keri Ramsey (K)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.
Center for Rare Childhood Disorders (C4RCD), Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Kamawela Leka (K)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Anna Abraham (A)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Emma Lieberman (E)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Katie Hassett (K)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Sai Potu (S)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Natasha Rudy (N)

Department of Genetics, University of Alabama at Birmingham, Birmingham, Alabama, USA.

Kirstin Smith (K)

Department of Genetics, University of Alabama at Birmingham, Birmingham, Alabama, USA.

Fady M Mikhail (FM)

Department of Genetics, University of Alabama at Birmingham, Birmingham, Alabama, USA.

Kirstin G Monaghan (KG)

GeneDx, Gaithersburg, Maryland, USA.

Andrea Hendershot (A)

GeneDx, Gaithersburg, Maryland, USA.

Jeroen Mourmans (J)

Deventer Hospital, Deventer, The Netherlands.

Maria Descartes (M)

Department of Genetics, University of Alabama at Birmingham, Birmingham, Alabama, USA.

Matthew J Huentelman (MJ)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.
Center for Rare Childhood Disorders (C4RCD), Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Jennifer Sills (J)

CSNK2A1 Foundation, San Francisco, California, USA.

Sampath Rangasamy (S)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.
Center for Rare Childhood Disorders (C4RCD), Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Vinodh Narayanan (V)

Neurogenomics Division, Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.
Center for Rare Childhood Disorders (C4RCD), Translational Genomics Research Institute (TGen), Phoenix, Arizona, USA.

Classifications MeSH