Association between common cardiovascular risk factors and clinical phenotype in patients with hypertrophic cardiomyopathy from the European Society of Cardiology (ESC) EurObservational Research Programme (EORP) Cardiomyopathy/Myocarditis registry.


Journal

European heart journal. Quality of care & clinical outcomes
ISSN: 2058-1742
Titre abrégé: Eur Heart J Qual Care Clin Outcomes
Pays: England
ID NLM: 101677796

Informations de publication

Date de publication:
13 12 2022
Historique:
received: 04 01 2022
revised: 02 02 2022
accepted: 04 02 2022
pubmed: 10 2 2022
medline: 15 12 2022
entrez: 9 2 2022
Statut: ppublish

Résumé

The interaction between common cardiovascular risk factors (CVRF) and hypertrophic cardiomyopathy (HCM) is poorly studied. We sought to explore the relation between CVRF and the clinical characteristics of patients with HCM enrolled in the EURObservational Research Programme (EORP) Cardiomyopathy registry. 1739 patients with HCM were studied. The relation between hypertension (HT), diabetes (DM), body mass index (BMI), and clinical traits was analysed. Analyses were stratified according to the presence or absence of a pathogenic variant in a sarcomere gene. The prevalence of HT, DM, and obesity (Ob) was 37, 10, and 21%, respectively. HT, DM, and Ob were associated with older age (P<0.001), less family history of HCM (HT and DM P<0.001), higher New York Heart Association (NYHA) class (P<0.001), atrial fibrillation (HT and DM P<0.001; Ob p = 0.03) and LV (left ventricular) diastolic dysfunction (HT and Ob P<0.001; DM P = 0.003). Stroke was more frequent in HT (P<0.001) and mutation-positive patients with DM (P = 0.02). HT and Ob were associated with higher provocable LV outflow tract gradients (HT P<0.001, Ob P = 0.036). LV hypertrophy was more severe in Ob (P = 0.018). HT and Ob were independently associated with NYHA class (OR 1.419, P = 0.017 and OR 1.584, P = 0.004, respectively). Other associations, including a higher proportion of females in HT and of systolic dysfunction in HT and Ob, were observed only in mutation-positive patients. Common CVRF are associated with a more severe HCM phenotype, suggesting a proactive management of CVRF should be promoted. An interaction between genotype and CVRF was observed for some traits.

Identifiants

pubmed: 35138368
pii: 6524906
doi: 10.1093/ehjqcco/qcac006
pmc: PMC9745665
doi:

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

42-53

Subventions

Organisme : Medical Research Council
ID : MR/T024062/1
Pays : United Kingdom
Organisme : Medical Research Council
ID : MR/T005181/1
Pays : United Kingdom

Investigateurs

Christopher Peter Gale (CP)
Branko Beleslin (B)
Andrzej Budaj (A)
Ovidiu Chioncel (O)
Nikolaos Dagres (N)
Nicolas Danchin (N)
David Erlinge (D)
Jonathan Emberson (J)
Michael Glikson (M)
Alastair Gray (A)
Meral Kayikcioglu (M)
Aldo Maggioni (A)
Klaudia Vivien Nagy (KV)
Aleksandr Nedoshivin (A)
Anna-Sonia Petronio (AS)
Jolien Roo Hesselink (JR)
Lars Wallentin (L)
Uwe Zeymer (U)
Alida Caforio (A)
Juan Ramon Gimeno Blanes (JRG)
Philippe Charron (P)
Perry Elliott (P)
Juan Pablo Kaski (JP)
Aldo P Maggioni (AP)
Luigi Tavazzi (L)
Michal Tendera (M)
S Komissarova (S)
N Chakova (N)
S Niyazova (S)
A Linhart (A)
P Kuchynka (P)
T Palecek (T)
J Podzimkova (J)
M Fikrle (M)
E Nemecek (E)
H Bundgaard (H)
J Tfelt-Hansen (J)
J Theilade (J)
J J Thune (JJ)
A Axelsson (A)
J Mogensen (J)
F Henriksen (F)
T Hey (T)
S K Nielsen (SK)
L Videbaek (L)
S Andreasen (S)
H Arnsted (H)
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Informations de copyright

© The Author(s) 2022. Published by Oxford University Press on behalf of the European Society of Cardiology.

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Auteurs

Luis R Lopes (LR)

Serviço de Cardiologia, Hospital Garcia de Orta, Av. Torrado da Silva, Almada 2805-267, Portugal.
Institute of Cardiovascular Science, University College London, Gower St, London WC1E 6BT, UK.
St. Bartholomew's Hospital, Barts Heart Centre, Barts Health NHS Trust, Whitechapel Rd, London E1 1BB, UK.

Maria-Angela Losi (MA)

Department of Advanced Biomedical Sciences, University Federico II, Corso Umberto I, 40, Naples 80138, Italy.

Nabeel Sheikh (N)

Department of Cardiology and Division of Cardiovascular Sciences, Guy's and St. Thomas' Hospitals and King's College London, Strand, London WC2R 2LS, UK.

Cécile Laroche (C)

EORP, European Society of Cardiology, Sophia-Antipolis, France.

Philippe Charron (P)

APHP, Centre de Référence des Maladies Cardiaques Héréditaires, Assistance Publique-Hôpitaux de Paris, ICAN, Hôpital Pitié-Salpêtrière, 47-83 Bd de l'Hôpital, Paris 75013, France.
Sorbonne Université, Inserm UMR1166, 15-21 Rue de l'École de Médecine, Paris 75006, France.

Juan Gimeno (J)

Hospital Clínico Universitario Virgen de la Arrixaca, Ctra. Madrid-Cartagena, Murcia 30120 El, Spain.

Juan P Kaski (JP)

Institute of Cardiovascular Science, University College London, Gower St, London WC1E 6BT, UK.
Centre for Inherited Cardiovascular Diseases, Great Ormond Street Hospital, London WC1N 3JH, UK.

Aldo P Maggioni (AP)

EORP, European Society of Cardiology, Sophia-Antipolis, France.
Maria Cecilia Hospital, GVM Care&Research, Via Corriera, 1, Cotignola 48033 RA, Italy.

Luigi Tavazzi (L)

Maria Cecilia Hospital, GVM Care&Research, Via Corriera, 1, Cotignola 48033 RA, Italy.

Eloisa Arbustini (E)

Centre for Inherited Cardiovascular Diseases, Fondazione IRCCS Policlinico San Matteo, Viale Camillo Golgi, Pavia 27100, Italy.

Dulce Brito (D)

Serviço de Cardiologia, Centro Hospitalar Universitário Lisboa Norte, Lisbon 1169-050, Portugal.
CCUL, Faculdade de Medicina, Universidade de Lisboa, Av. Prof. Egas Moniz MB, Lisbon 1649-028, Portugal.

Jelena Celutkiene (J)

Clinic of Cardiac and Vascular Diseases, Institute of Clinical Medicine, Faculty of Medicine, Vilnius University, Universiteto g. 3, Vilnius 01513, Lithuania.
State Research Institute Centre for Innovative Medicine, Vilnius, Lithuania.

Albert Hagege (A)

Assistance Publique-Hôpitaux de Paris, Hôpital Européen Georges Pompidou, Département de Cardiologie, Paris, France & Université Paris Descartes, Sorbonne Paris Cité, Paris 75006, France.

Ales Linhart (A)

2nd Department of Internal Cardiovascular Medicine, General University Hospital and First Medical Faculty, Charles University, Opletalova 38, Prague 110 00, Czech Republic.

Jens Mogensen (J)

Department of Cardiology, Odense University Hospital, J. B. Winsløws Vej 4, Odense 5000, Denmark.

José Manuel Garcia-Pinilla (JM)

Unidad de Insuficiencia Cardiaca y Cardiopatías Familiares. Servicio de Cardiología. Hospital Universitario Virgen de la Victoria. IBIMA. Málaga and Ciber-Cardiovascular. Instituto de Salud Carlos III. Madrid, Spain.

Tomas Ripoll-Vera (T)

Inherited Cardiovascular Disease Unit Son Llatzer University Hospital & IdISBa, Palma de Mallorca, Spain.

Hubert Seggewiss (H)

Universitätsklinikum Würzburg, Deutsches Zentrum für Herzinsuffizienz (DZHI), Comprehensive Heart Failure Center (CHFC), Am Schwarzenberg 15, Haus 15A, 97078 Wurzburg, Germany.

Eduardo Villacorta (E)

Member of National Centers of expertise for familial cardiopathies (CSUR), Cardiology Department, University Hospital of Salamanca. Institute of Biomedical Research of Salamanca (IBSAL), CIBERCV, Salamanca, Spain.

Alida Caforio (A)

Cardiology, Department of Cardiological, Thoracic and Vascular Sciences and Public Health, University of Padova, Via VIII Febbraio, 2, Padova 35122, Italy.

Perry M Elliott (PM)

Institute of Cardiovascular Science, University College London, Gower St, London WC1E 6BT, UK.
St. Bartholomew's Hospital, Barts Heart Centre, Barts Health NHS Trust, Whitechapel Rd, London E1 1BB, UK.

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