Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation.
Journal
Case reports in pathology
ISSN: 2090-6781
Titre abrégé: Case Rep Pathol
Pays: United States
ID NLM: 101576609
Informations de publication
Date de publication:
2021
2021
Historique:
received:
29
11
2020
revised:
03
04
2021
accepted:
05
05
2021
entrez:
31
5
2021
pubmed:
1
6
2021
medline:
1
6
2021
Statut:
epublish
Résumé
Primary leiomyosarcomas (LMS) of vascular origin are rare tumors, and more than half of the cases arise in the inferior vena cava (IVC). Primary LMS of the renal vein are extremely rare tumors with only a few cases reported in the literature. Their diagnosis is made only by pathological features. Histologically, they are made of atypical spindle-shaped cells arranged in long intersecting fascicles. Tumor cells stain positive for myogenic markers in immunohistochemistry. Standard treatment consists of radical nephrectomy followed by chemotherapy and/or radiotherapy. Because of insufficient histological data and follow-up, the prognosis factors are not well identified. Overall prognosis of renal vein LMS is poor. We report here an exceptional case of a huge LMS of the right renal vein mimicking a primitive renal cell carcinoma, occurring in a 56-year-old male patient.
Identifiants
pubmed: 34055441
doi: 10.1155/2021/6637533
pmc: PMC8133846
doi:
Types de publication
Case Reports
Langues
eng
Pagination
6637533Informations de copyright
Copyright © 2021 Amal Fekkar et al.
Déclaration de conflit d'intérêts
All authors declare no conflicts of interest.
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