Aberrant Expression of High Mobility Group Box Protein 1 in the Idiopathic Inflammatory Myopathies.

HMGB1 idiopathic inflammatory myopathy immune-mediated necrotising myopathy immune-mediated necrotizing myopathy inclusion body myositis myositis necrotising autoimmune myopathy necrotizing autoimmune myopathy

Journal

Frontiers in cell and developmental biology
ISSN: 2296-634X
Titre abrégé: Front Cell Dev Biol
Pays: Switzerland
ID NLM: 101630250

Informations de publication

Date de publication:
2020
Historique:
received: 04 02 2020
accepted: 17 03 2020
entrez: 5 5 2020
pubmed: 5 5 2020
medline: 5 5 2020
Statut: epublish

Résumé

High Mobility Group Box Protein 1 (HMGB1) is a DNA-binding protein that exerts inflammatory or pro-repair effects upon translocation from the nucleus. We postulate aberrant HMGB1 expression in immune-mediated necrotising myopathy (IMNM). Herein, we compare HMGB1 expression (serological and sarcoplasmic) in patients with IMNM with that of other myositis subtypes using immunohistochemistry and ELISA. IMNM ( Aberrant HMGB1 expression occurs in myositis patients and correlates with weakness. A unique expression profile of elevated sarcoplasmic and serum HMGB1 was detected in IMNM.

Identifiants

pubmed: 32363191
doi: 10.3389/fcell.2020.00226
pmc: PMC7180187
doi:

Types de publication

Journal Article

Langues

eng

Pagination

226

Informations de copyright

Copyright © 2020 Day, Otto, Cash, Eldi, Hissaria, Proudman, Limaye and Hayball.

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Auteurs

Jessica Day (J)

Experimental Therapeutics Laboratory, University of South Australia Cancer Research Institute, Adelaide, SA, Australia.
School of Pharmacy and Medical Sciences, University of South Australia, Adelaide, SA, Australia.
Royal Adelaide Hospital, Adelaide, SA, Australia.

Sophia Otto (S)

Royal Adelaide Hospital, Adelaide, SA, Australia.
SA Pathology, Adelaide, SA, Australia.

Kathy Cash (K)

SA Pathology, Adelaide, SA, Australia.

Preethi Eldi (P)

Experimental Therapeutics Laboratory, University of South Australia Cancer Research Institute, Adelaide, SA, Australia.
School of Pharmacy and Medical Sciences, University of South Australia, Adelaide, SA, Australia.

Pravin Hissaria (P)

Royal Adelaide Hospital, Adelaide, SA, Australia.
SA Pathology, Adelaide, SA, Australia.

Susanna Proudman (S)

Royal Adelaide Hospital, Adelaide, SA, Australia.
Discipline of Medicine, University of Adelaide, Adelaide, SA, Australia.

Vidya Limaye (V)

Royal Adelaide Hospital, Adelaide, SA, Australia.
Discipline of Medicine, University of Adelaide, Adelaide, SA, Australia.

John D Hayball (JD)

Experimental Therapeutics Laboratory, University of South Australia Cancer Research Institute, Adelaide, SA, Australia.
School of Pharmacy and Medical Sciences, University of South Australia, Adelaide, SA, Australia.
Robinson Research Institute and Adelaide Medical School, University of Adelaide, Adelaide, SA, Australia.

Classifications MeSH