Neonatal Soft Tissue Sarcoma with YWHAE-NUTM2B Fusion.

Cancer biology Chemotherapy Fusion transcript Neonatal Sarcoma

Journal

Case reports in oncology
ISSN: 1662-6575
Titre abrégé: Case Rep Oncol
Pays: Switzerland
ID NLM: 101517601

Informations de publication

Date de publication:
Historique:
received: 18 07 2019
accepted: 18 07 2019
entrez: 24 9 2019
pubmed: 24 9 2019
medline: 24 9 2019
Statut: epublish

Résumé

Neonatal soft tissues sarcoma is a rare entity that comprises heterogeneous types of tumors. In this article we describe a neonatal case of round-cell sarcoma with an YWHAE-NUTM2B fusion gene. The patient was treated just after birth with neoadjuvant chemotherapy, then surgical resection, but evolution was quickly fatal. This fusion transcript has been reported in endometrial stromal sarcomas and clear cells renal sarcomas but its description in small round-cell sarcomas is recent. To our knowledge, this is the first case report describing this translocation in a newborn patient with soft tissues sarcoma and its clinical tumoral evolution.

Identifiants

pubmed: 31543780
doi: 10.1159/000502227
pii: cro-0012-0631
pmc: PMC6738155
doi:

Types de publication

Case Reports

Langues

eng

Pagination

631-638

Déclaration de conflit d'intérêts

The authors have no conflicts of interest to report.

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Auteurs

Maylis Guizard (M)

Department of Pediatric and Adolescent Oncology, Centre Leon Berard, Lyon, France.

Marie Karanian (M)

Department of Biopathology, Centre Léon Berard, Lyon, France.
Univ Lyon, Université Claude Bernard Lyon 1, INSERM 1052, CNRS 5286, Research Cancer center of Lyon, Centre Léon Bérard, Lyon, France.

Frédérique Dijoud (F)

Institut Multisite de Pathologie, Hopital Femme Mere Enfant, Bron, France.

Amine Bouhamama (A)

Department of Radiology, Centre Léon Berard, Lyon, France.

Cécile Faure-Conter (C)

Department of Pediatric and Adolescent Oncology, Centre Leon Berard, Lyon, France.

Frédéric Hameury (F)

Department of Pediatric Surgery, Hopital Femme Mere Enfant, Bron, France.

Franck Tirode (F)

Univ Lyon, Université Claude Bernard Lyon 1, INSERM 1052, CNRS 5286, Research Cancer center of Lyon, Centre Léon Bérard, Lyon, France.

Nadège Corradini (N)

Department of Pediatric and Adolescent Oncology, Centre Leon Berard, Lyon, France.

Classifications MeSH